文献类型：期刊文献

英文题名：Anomalous origin of a right pulmonary artery identified with echocardiography combined with CT: a case in a juvenile patient

作者：Li, Yan-ling[1,2];Xie, Ping[1,2];Wei, Jia[2];Guo, Zhao-xia[2]

第一作者：Li, Yan-ling;李亚玲;李玉兰;李亚隆

通信作者：Guo, ZX[1]

机构：[1]Gansu Univ Chinese Med, Sch Tradit Chinese & Western Med, Lanzhou 730000, Peoples R China;[2]Gansu Prov Hosp, Dept Cardiol, Lanzhou 730000, Gansu, Peoples R China

第一机构：甘肃中医药大学

通信机构：[1]corresponding author), Gansu Prov Hosp, Dept Cardiol, Lanzhou 730000, Gansu, Peoples R China.

年份：2025

卷号：20

期号：1

外文期刊名：JOURNAL OF CARDIOTHORACIC SURGERY

收录：;Scopus(收录号：2-s2.0-85218233174);WOS:【SCI-EXPANDED(收录号:WOS:001415448900003)】；

基金：A grant from the General Project of the Natural Science Foundation of Gansu Province (22JR5RA665, 22JR11RA254) supported this study.

语种：英文

外文关键词：Anomalous origin of the pulmonary artery; Congenital heart malformation; Transthoracic echocardiography

摘要：An anomalous origin of the pulmonary artery (AOPA) from the ascending aorta is a relatively rare but important cardiac malformation that frequently involves the right pulmonary artery (RPA). Its clinical manifestations depend mainly on the associated significant pulmonary hypertension, with an extremely high mortality rate in the first year of life. Here, we present a rare survival case of an 11-year-old child with the disease, who was hospitalized due to intermittent abdominal pain, but without any apparent signs of chest tightness or shortness of breath. The low oxygen saturation as discovered during the physical examination. Subsequent examination with transthoracic echocardiography (TTE) and pulmonary artery computed tomography angiography (CTA) revealed this unexpected congenital malformation. Although the estimated mean pulmonary artery pressure (MAP) from the TTE was 51 mmHg, which seemed to contraindicate corrective cardiac surgery, the limitations of TTE were considered. Consequently, after multidisciplinary consultation, surgical intervention was ultimately decided upon, resulting in a favorable prognosis for the patient. This case provides a new insight for clinicians in the diagnosis and treatment of complex congenital heart diseases.